Duodenal atresia is the congenital absence or complete closure of a portion of the lumen of the duodenum. It causes increased levels of amniotic fluid during. Duodenal atresia or stenosis is a rare congenital digestive disorder that usually occurs for no apparent reason (sporadically). However, a few. A collection of disease information resources and questions answered by our Genetic and Rare Diseases Information Specialists for Duodenal atresia.

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This depends on your baby’s recovery from the operation as well as the length of time that is taken to achieve complete oral feeding. Because every pregnancy is different, this may not be applicable to all cases, especially if there are additional defects. Duodenal atresia can result in an increase in the amniotic fluid around the baby known as atrexia which may lead to an early delivery.

Nelson Textbook of Pediatrics. Annular pancreas Accessory pancreas Johanson—Blizzard syndrome Pancreas divisum. Intestinal atresia Duodenal atresia Meckel’s diverticulum Hirschsprung’s disease Intestinal malrotation Dolichocolon Enteric duplication cyst. Treatment includes suctioning out any fluid that is trapped in the stomach, providing fluids intravenously, and surgical repair of the intestinal closure. An X-ray of the abdomen shows two large air filled spaces, the so-called “double bubble” sign.

Associated abnormalities have been found in some infants with duodenal atresia or duodenal stenosis.

Duodenal atresia

acalah It should be possible atresiq you to deliver your baby in the normal way unless there are other reasons for requiring a Caesarean section. In most cases the stay is about two weeks. They may wax and wane not appearing for weeks, months, or years. Because the amniotic fluid is normally swallowed and digested by the fetus, duodenal atresia can cause an increase in fluid in the amniotic sac, hydramnios. Following discharge your baby will be seen in the outpatients department by members of the surgical team, where help and advice will be available to you.


Symptoms of partial duodenal atresja vary depending on the severity. Oesophageal atresia and tracheo-oesophageal fistula TOF. External links Down syndrome information.

Because too little food reaches the intestines, constipation is a frequent complication, as is failure of the infant to gain weight. Journal of Pediatric Surgery. Gastrointestinal tract disorders Congenital disorders of digestive system. This abnormality causes a portion of the small intestine the jejunal to twist around one of the arteries of the colon.

Radiography shows a distended stomach and distended duodenum, which are separated by the pyloric valve, a finding described as the double-bubble sign. Calkins CM, Karrer F. The development of forceful vomiting projectile immediately after eating or when the stomach is filled is one of the first symptoms. A child diagnosed with duodenal atresia will require an operation to address the problem and may stay in the hospital for several ateesia.

The appearance of this condition resembles a Christmas tree or apple peel when viewed by a surgeon. Appointment available in next 7 days. Twenty to thirty percent of individuals affected with these disorders have Down syndrome and twenty-two percent have heart disease.

Atresias occurring distal to the duodenum are usually caused by vascular accidents or ischemic insult, such as jejunoileal atresia. Since the closure of the duodenum is complete in duodenal atresia, no air is seen in the distal duodenum. Inguinal hernia in boys. The ultimate judgement regarding a particular clinical procedure or treatment must be made by the clinician in the light of the clinical data presented by the patient and the diagnostic or treatment options available.

Duodenal atresia is the congenital absence or complete closure of a portion of the lumen of the duodenum.

The overall outcomes for most duodenal atresias are excellent depending on the presence of additional problems. The severity and treatment of these complications should be discussed with your pediatric surgeon if they occur.


Early treatment includes removing fluids from the stomach via a nasogastric tubeand providing fluids intravenously. Once the baby has been fully assessed, a pediatric surgeon will evaluate your newborn.

Although there are many other causes of hydramnios, this may be a first sign of a duodenal atresia.

Duodenal atresia occurs between 1 in 1, and 1 in 5, live births. From Wikipedia, the free encyclopedia. Additional tests may be required to confirm a suspected diagnosis of duodenal atresia. If complications arise, the obstetrician may decide to induce delivery earlier than the expected due duorenum. Because of this association, newborns are often tested for other problems such a heart defects.

Duodenal Atresia or Stenosis – NORD (National Organization for Rare Disorders)

Babies with duodenal atresia vomit soon after birth and the vomit is usually bile-stained greenafter which:. They represent recognised methods and techniques of clinical practice, based on published evidence. It should be possible for the baby to grow quite normally on this form of feeding while the bowel is recovering. Duodenal atresia and duodenal stenosis are abnormalities in which there is an absence or complete closure atresia in the first part of the small intestines duodenum or narrowing stenosis of the duodenum.

Rare Disease Database

The fetal team will closely evaluate your fetus with duodenal atresia and help determine the best course of treatment. D ICD – In most cases, a child with duodenal atresia will be born xuodenum any immediate problems.

J Med Assoc Thai.